{"id":4087,"date":"2025-02-06T05:59:41","date_gmt":"2025-02-06T04:59:41","guid":{"rendered":"https:\/\/rvh-synergie.org\/actualites\/les-chercheurs-decouvrent-la-source-de-cellules-qui-contribuent-a-la-fibrose-pulmonaire\/"},"modified":"2025-02-06T05:59:41","modified_gmt":"2025-02-06T04:59:41","slug":"les-chercheurs-decouvrent-la-source-de-cellules-qui-contribuent-a-la-fibrose-pulmonaire","status":"publish","type":"post","link":"https:\/\/rvh-synergie.org\/actualites\/les-chercheurs-decouvrent-la-source-de-cellules-qui-contribuent-a-la-fibrose-pulmonaire\/","title":{"rendered":"Les chercheurs d\u00e9couvrent la source de cellules qui contribuent \u00e0 la fibrose pulmonaire"},"content":{"rendered":"<div>\n<div class=\"article-gallery lightGallery\">\n<div data-thumb=\"https:\/\/scx1.b-cdn.net\/csz\/news\/tmb\/2025\/found-the-source-of-ce-1.jpg\" data-src=\"https:\/\/scx2.b-cdn.net\/gfx\/news\/2025\/found-the-source-of-ce-1.jpg\" data-sub-html=\"Lung organoids subjected to conditions that promote pulmonary fibrosis helped researchers identify the healthy cells that transition into cells that damage the lung. Identification of the source of pathological cells could lead to better treatments for the disease. Credit: Jianwen Que\/Columbia University Vagelos College of Physicians and Surgeons.\">\n<figure class=\"article-img\">\n<\/figure><\/div>\n<\/div>\n<p>Les chercheurs essaient depuis des d\u00e9cennies pour arr\u00eater les cellules qui endommagent le poumon chez les personnes atteintes de fibrose pulmonaire. Maintenant, une \u00e9quipe de chercheurs de Columbia et de l&rsquo;UCSD a peut-\u00eatre trouv\u00e9 une solution intelligente qui \u00e9vite la difficult\u00e9 d&rsquo;arr\u00eater les cellules et bloque simplement la cr\u00e9ation des cellules.<\/p>\n<p>Dans leur nouvelle \u00e9tude, publi\u00e9e dans <i>Nature<\/i>les chercheurs ont d\u00e9couvert les origines des cellules destructrices &#8211; qui a perplexe le champ pendant des ann\u00e9es &#8211; puis a identifi\u00e9 un moyen de fermer leur production.<\/p>\n<p>\u00ab\u00a0Ne pas conna\u00eetre les sources de ces cellules pathologiques a vraiment entrav\u00e9 le d\u00e9veloppement de th\u00e9rapies qui pourraient mettre un terme \u00e0 cette maladie, il y a donc eu un effort intense pour les trouver\u00a0\u00bb, explique Jianwen Que, professeur de m\u00e9decine \u00e0 Columbia University Vacelos College of Physicians et les chirurgiens, qui ont co-dirig\u00e9 l&rsquo;\u00e9tude. \u00ab\u00a0Cela peut prendre des ann\u00e9es pour traduire nos r\u00e9sultats, mais nous esp\u00e9rons qu&rsquo;ils m\u00e8neront \u00e0 des traitements plus efficaces.\u00a0\u00bb<\/p>\n<h2>Qu&rsquo;est-ce que la fibrose pulmonaire?<\/h2>\n<p>La fibrose pulmonaire peut se d\u00e9velopper apr\u00e8s une blessure pulmonaire, y compris le Covid-19, mais la plupart des cas surviennent sans aucune cause claire.<\/p>\n<p>Une fois diagnostiqu\u00e9, la maladie endommage rapidement le poumon et les patients meurent g\u00e9n\u00e9ralement d&rsquo;une insuffisance respiratoire dans les deux \u00e0 cinq ans. Deux m\u00e9dicaments approuv\u00e9s au cours de la derni\u00e8re d\u00e9cennie peuvent ralentir la maladie mais ne peuvent pas l&rsquo;arr\u00eater.<\/p>\n<p>Les cellules qui causent les dommages pulmonaires se d\u00e9veloppent \u00e0 partir de cellules pulmonaires saines mais sont entra\u00een\u00e9es \u00e0 d\u00e9poser des quantit\u00e9s excessives de tissu cicatriciel dans le poumon. \u00ab\u00a0Ironiquement, ces cellules essaient de r\u00e9parer les blessures pulmonaires, mais elles vont trop loin\u00a0\u00bb, dit Que. \u00ab\u00a0Le tissu cicatriciel qu&rsquo;ils produisent enrasse de plus en plus les sacs d&rsquo;air du poumon dans une matrice raide. Le poumon devient litt\u00e9ralement trop difficile \u00e0 respirer.\u00a0\u00bb<\/p>\n<div class=\"article-gallery lightGallery\">\n<div data-thumb=\"https:\/\/scx1.b-cdn.net\/csz\/news\/tmb\/2025\/found-the-source-of-ce.jpg\" data-src=\"https:\/\/scx2.b-cdn.net\/gfx\/news\/hires\/2025\/found-the-source-of-ce.jpg\" data-sub-html=\"&lt;i&gt;Lepr&lt;\/i&gt;-expressing lung mesenchymal cells generate pathological fibroblasts during pulmonary fibrosis. Credit: &lt;i&gt;Nature&lt;\/i&gt; (2025). DOI: 10.1038\/s41586-024-08542-2\">\n<figure class=\"article-img text-center\">\n            <img decoding=\"async\" src=\"https:\/\/rvh-synergie.org\/actualites\/wp-content\/uploads\/2025\/02\/1738817981_755_Les-chercheurs-decouvrent-la-source-de-cellules-qui-contribuent-a.jpg\" alt=\"Trouv\u00e9: La source de cellules qui contribuent \u00e0 la fibrose pulmonaire\" title=\"Les cellules m\u00e9senchymateuses pulmonaires exprimant le LEPR g\u00e9n\u00e8rent des fibroblastes pathologiques pendant la fibrose pulmonaire. Cr\u00e9dit: Nature (2025). Doi: 10.1038 \/ s41586-024-08542-2\"><br \/>\n                     <\/figure>\n<\/p><\/div>\n<\/div>\n<h2>Le tra\u00e7age am\u00e9lior\u00e9 r\u00e9v\u00e8le des origines cellulaires<\/h2>\n<p>De nombreux types de cellules pulmonaires saines ont \u00e9t\u00e9 propos\u00e9es comme sources des cellules pathologiques dans la fibrose pulmonaire mais une preuve d\u00e9finitive &#8211; possible avec le suivi de la lign\u00e9e cellulaire &#8211; a manqu\u00e9.<\/p>\n<p>Que et ses coll\u00e8gues ont utilis\u00e9 des m\u00e9thodes de suivi avanc\u00e9es qui utilisent le s\u00e9quen\u00e7age d&rsquo;ARN de cellules individuelles pour une identification plus pr\u00e9cise. Ces techniques n&rsquo;avaient pas \u00e9t\u00e9 syst\u00e9matiquement d\u00e9ploy\u00e9es auparavant, car les lign\u00e9es de souris pour \u00e9tudier la contribution possible de toutes les sources cellulaires suspect\u00e9es n&rsquo;\u00e9taient pas disponibles.<\/p>\n<p>Avec de nouvelles lign\u00e9es de souris cr\u00e9\u00e9es pour l&rsquo;\u00e9tude, les chercheurs ont constat\u00e9 que les cellules pathologiques jaillissent des fibroblastes normaux, marqu\u00e9s de r\u00e9cepteurs de leptine, dans les sacs a\u00e9riens du poumon.<\/p>\n<h2>Annuler les cellules pathologiques<\/h2>\n<p>Avec une source majeure de cellules pathologiques identifi\u00e9es, les chercheurs ont ensuite pu apprendre qu&rsquo;un facteur de transcription appel\u00e9 RUNX2 joue un r\u00f4le essentiel dans la conversion des fibroblastes normaux en cellules pathologiques.<\/p>\n<p>La d\u00e9sactivation du g\u00e8ne RUNX2 chez les souris a bloqu\u00e9 la conversion et r\u00e9duit la quantit\u00e9 de tissu fibrotique dans le poumon d&rsquo;environ 50%. Les chercheurs ont \u00e9galement trouv\u00e9 des preuves que Runx2 joue un r\u00f4le important dans les fibroblastes pathologiques tir\u00e9s de patients atteints de fibrose pulmonaire.<\/p>\n<p>\u00ab\u00a0Dans l&rsquo;ensemble, notre \u00e9tude sugg\u00e8re que RunX2 est une cible th\u00e9rapeutique potentielle pour pr\u00e9venir ou traiter la fibrose pulmonaire\u00a0\u00bb, dit Que, \u00ab\u00a0et donne aux chercheurs une plate-forme pour trouver encore plus d&rsquo;opportunit\u00e9s pour pr\u00e9venir la progression agressive de cette maladie.\u00a0\u00bb<\/p>\n<p>                                        <!-- print only --><\/p><\/div>\n","protected":false},"excerpt":{"rendered":"<p>Les chercheurs essaient depuis des d\u00e9cennies pour arr\u00eater les cellules qui endommagent le poumon chez<\/p>\n","protected":false},"author":1,"featured_media":4088,"comment_status":"closed","ping_status":"","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[86],"tags":[1622,288,1525,364,654,49,2276,193,579],"class_list":["post-4087","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-les-maladies","tag-cellules","tag-chercheurs","tag-contribuent","tag-decouvrent","tag-fibrose","tag-les","tag-pulmonaire","tag-qui","tag-source","generate-columns","tablet-grid-50","mobile-grid-100","grid-parent","grid-50","resize-featured-image"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.4 - 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