{"id":3707,"date":"2025-01-22T01:57:01","date_gmt":"2025-01-22T00:57:01","guid":{"rendered":"https:\/\/rvh-synergie.org\/actualites\/la-recherche-elucide-le-mecanisme-derriere-la-degenerescence-lobaire-frontotemporale\/"},"modified":"2025-01-22T01:57:03","modified_gmt":"2025-01-22T00:57:03","slug":"la-recherche-elucide-le-mecanisme-derriere-la-degenerescence-lobaire-frontotemporale","status":"publish","type":"post","link":"https:\/\/rvh-synergie.org\/actualites\/la-recherche-elucide-le-mecanisme-derriere-la-degenerescence-lobaire-frontotemporale\/","title":{"rendered":"La recherche \u00e9lucide le m\u00e9canisme derri\u00e8re la d\u00e9g\u00e9n\u00e9rescence lobaire frontotemporale"},"content":{"rendered":"<div>\n<div class=\"article-gallery lightGallery\">\n<div data-thumb=\"https:\/\/scx1.b-cdn.net\/csz\/news\/tmb\/2025\/elucidation-of-the-mec.jpg\" data-src=\"https:\/\/scx2.b-cdn.net\/gfx\/news\/2025\/elucidation-of-the-mec.jpg\" data-sub-html=\"Alterations in the morphology of mushroom bodies in VCP\/TER94 knockdown flies were rescued by the coexpression of wild-type VCP\/TER94, but to a lesser extent by the coexpression of disease-associated mutant VCP\/TER94. Credit: Dr. Masaaki Sone\">\n<figure class=\"article-img\">\n<\/figure><\/div>\n<\/div>\n<p>Les chercheurs ont d\u00e9couvert le m\u00e9canisme sous-jacent \u00e0 la d\u00e9g\u00e9n\u00e9rescence lobaire frontotemporale (FTLD) provoqu\u00e9e par des variantes du g\u00e8ne de la prot\u00e9ine contenant de la valosine (VCP). Leur \u00e9tude, qui a utilis\u00e9 un mod\u00e8le de mouche des fruits, r\u00e9v\u00e8le des informations cl\u00e9s sur la maladie, jetant ainsi les bases d\u2019un futur d\u00e9veloppement th\u00e9rapeutique.<\/p>\n<p>Les r\u00e9sultats sont publi\u00e9s dans <i>Mod\u00e8les et m\u00e9canismes de maladies.<\/i> Les groupes de recherche \u00e9taient dirig\u00e9s par le professeur agr\u00e9g\u00e9 Masaki Sone de la Facult\u00e9 des sciences de l&rsquo;Universit\u00e9 de Toho et le professeur Hitoshi Okazawa de l&rsquo;Institut des sciences de Tokyo et de l&rsquo;Universit\u00e9 de Maastricht aux Pays-Bas.<\/p>\n<p>Les m\u00e9canismes sous-jacents \u00e0 la FTLD sont provoqu\u00e9s par des variantes du g\u00e8ne VCP. La prolif\u00e9ration anormale de cellules souches neurales au cours du d\u00e9veloppement neuronal, d\u00e9clench\u00e9e par la perte de la fonction du g\u00e8ne VCP, entra\u00eene des sympt\u00f4mes neurod\u00e9g\u00e9n\u00e9ratifs.<\/p>\n<p>La FTLD est une cause majeure de d\u00e9mence, avec une pr\u00e9valence juste derri\u00e8re celle de la maladie d&rsquo;Alzheimer et de la d\u00e9mence \u00e0 corps de Lewy. On sait que les mutations du g\u00e8ne VCP provoquent une FTLD h\u00e9r\u00e9ditaire. Des \u00e9tudes collaboratives ant\u00e9rieures, notamment celles men\u00e9es par l&rsquo;\u00e9quipe du professeur Hitoshi Okazawa \u00e0 l&rsquo;Institut des sciences de Tokyo et l&rsquo;\u00e9quipe du professeur agr\u00e9g\u00e9 Masaki Sone \u00e0 l&rsquo;Universit\u00e9 de Toho, avaient identifi\u00e9 que les dommages \u00e0 l&rsquo;ADN au cours du stade f\u0153tal affectent l&rsquo;apparition de la FTLD apr\u00e8s des d\u00e9cennies d&rsquo;utilisation d&rsquo;un mod\u00e8le murin.<\/p>\n<p>Dans le nouveau travail, l&rsquo;\u00e9quipe a utilis\u00e9 un mod\u00e8le de mouche des fruits pour montrer que la perte de la fonction du g\u00e8ne VCP entra\u00eene une prolif\u00e9ration anormale de cellules souches neurales au cours du stade de d\u00e9veloppement. Cette anomalie a \u00e9t\u00e9 identifi\u00e9e comme une cause directe des sympt\u00f4mes neurod\u00e9g\u00e9n\u00e9ratifs. Ces r\u00e9sultats offrent des informations fondamentales pour le d\u00e9veloppement de nouveaux traitements pour le FTLD.<\/p>\n<p>                                        <!-- print only --><\/p><\/div>\n","protected":false},"excerpt":{"rendered":"<p>Les chercheurs ont d\u00e9couvert le m\u00e9canisme sous-jacent \u00e0 la d\u00e9g\u00e9n\u00e9rescence lobaire frontotemporale (FTLD) provoqu\u00e9e par<\/p>\n","protected":false},"author":1,"featured_media":3708,"comment_status":"closed","ping_status":"","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[86],"tags":[2870,2023,3628,3630,3629,1256,499],"class_list":["post-3707","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-les-maladies","tag-degenerescence","tag-derriere","tag-elucide","tag-frontotemporale","tag-lobaire","tag-mecanisme","tag-recherche","generate-columns","tablet-grid-50","mobile-grid-100","grid-parent","grid-50","resize-featured-image"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.4 - 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