{"id":14301,"date":"2026-02-21T23:11:05","date_gmt":"2026-02-21T22:11:05","guid":{"rendered":"https:\/\/rvh-synergie.org\/actualites\/quest-ce-qui-se-cache-derriere-la-maladie-nerveuse-incurable-sla\/"},"modified":"2026-02-21T23:11:07","modified_gmt":"2026-02-21T22:11:07","slug":"quest-ce-qui-se-cache-derriere-la-maladie-nerveuse-incurable-sla","status":"publish","type":"post","link":"https:\/\/rvh-synergie.org\/actualites\/quest-ce-qui-se-cache-derriere-la-maladie-nerveuse-incurable-sla\/","title":{"rendered":"Qu&rsquo;est-ce qui se cache derri\u00e8re la maladie nerveuse incurable SLA"},"content":{"rendered":"<p><!--$--><\/p>\n<div data-hk=\"00942120a20200\" class=\"Html-Block\" data-qa-article-content-text>\n<ul>\n<li><i>dans la vid\u00e9o : La star de \u00ab\u00a0Grey&rsquo;s Anatomy\u00a0\u00bb, Eric Dane, d\u00e9c\u00e8de \u00e0 seulement 53 ans<\/i><\/li>\n<\/ul>\n<p>Eric Dane est d\u00e9c\u00e9d\u00e9 \u00e0 l&rsquo;\u00e2ge de 53 ans des suites de la scl\u00e9rose lat\u00e9rale amyotrophique (SLA). Il n\u2019a rendu publique sa maladie que l\u2019ann\u00e9e derni\u00e8re.<\/p>\n<\/div>\n<div data-hk=\"00942120a20210\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>La star de \u00ab\u00a0Grey&rsquo;s Anatomy\u00a0\u00bb d\u00e9c\u00e8de de la SLA<\/h2>\n<p>La SLA est une maladie neurod\u00e9g\u00e9n\u00e9rative grave. Cela affecte principalement le syst\u00e8me nerveux moteur, comme l&rsquo;\u00e9crit la Soci\u00e9t\u00e9 allemande pour les patients musculaires. La SLA entra\u00eene une faiblesse musculaire progressive et une paralysie.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202204\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor Ad-Slot-FC\">\n<div class=\"Ad-Slot-FC-Container\">\n<div class=\"Ad-Slot-FC-Window\">\n<div id=\"ad-slot-mobile-hor-2\" data-orientation=\"hor\" data-index=\"2\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/div>\n<\/div>\n<\/aside>\n<div data-hk=\"00942120a20230\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Les sympt\u00f4mes les plus courants de la SLA<\/h2>\n<p>Les sympt\u00f4mes les plus courants sont<\/p>\n<\/div>\n<div data-hk=\"00942120a20240\" class=\"Html-Block\" data-qa-article-content-text>\n<ul>\n<li><strong>Faiblesse musculaire et atrophie (atrophie)<\/strong><\/li>\n<li><strong>contractions musculaires involontaires (fasciculations)<\/strong><\/li>\n<li><strong>crampes musculaires douloureuses<\/strong><\/li>\n<li><strong>Spasticit\u00e9 et augmentation des r\u00e9flexes<\/strong><\/li>\n<li><strong>Troubles des muscles de la parole, de la mastication et de la d\u00e9glutition<\/strong><\/li>\n<li><strong>faiblesse des muscles respiratoires<\/strong>ce qui peut entra\u00eener une insuffisance respiratoire<\/li>\n<li><strong>changements cognitifs<\/strong> (environ cinq pour cent des personnes concern\u00e9es d\u00e9veloppent une d\u00e9mence fronto-temporale accompagn\u00e9e de probl\u00e8mes de comportement)<\/li>\n<\/ul>\n<p>Les sensations sensorielles, telles que le toucher, l&rsquo;odorat, l&rsquo;ou\u00efe et la vue, sont conserv\u00e9es. La conscience et les capacit\u00e9s de r\u00e9flexion ne sont pas non plus affect\u00e9es. M\u00eame si la plupart des patients restent lucides, ils ne sont plus capables de communiquer \u00e0 mesure que la maladie progresse, selon le Centre allemand des maladies neurod\u00e9g\u00e9n\u00e9ratives (DZNE). <\/p>\n<\/div>\n<aside data-hk=\"00942120a202504\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-out\">\n<div id=\"ad-slot-mobile-out-1\" data-orientation=\"out\" data-index=\"1\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a20260\" class=\"Ad-Row\">\n<div class=\"Ad-Col col-lg-5\">\n<div data-hk=\"00942120a2026104\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-desktop Ad-Slot-ver\" role=\"region\" aria-label=\"Anzeige 1\">\n<div id=\"ad-slot-desktop-ver-1\" data-orientation=\"ver\" data-index=\"1\" data-slot=\"ad-slot\" data-device=\"desktop\"><\/div>\n<\/div>\n<\/div>\n<div class=\"Ad-Col col-lg-5\">\n<aside data-hk=\"00942120a2026204\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-desktop Ad-Slot-ver Ad-Slot-FC\">\n<div class=\"Ad-Slot-FC-Container\">\n<div class=\"Ad-Slot-FC-Window\">\n<div id=\"ad-slot-desktop-ver-2\" data-orientation=\"ver\" data-index=\"2\" data-slot=\"ad-slot\" data-device=\"desktop\"><\/div>\n<\/div>\n<\/div>\n<\/aside>\n<\/div>\n<\/div>\n<div data-hk=\"00942120a20270\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Quels sont les facteurs de risque<\/h2>\n<p>Les d\u00e9clencheurs et les facteurs de risque sont diff\u00e9rents. Joue comme \u00e7a<\/p>\n<\/div>\n<div data-hk=\"00942120a20280\" class=\"Html-Block\" data-qa-article-content-text>\n<ul>\n<li>la pr\u00e9disposition g\u00e9n\u00e9tique<\/li>\n<li>un travail physique intense ou<\/li>\n<li>Facteurs environnementaux (pesticides, infections)<\/li>\n<\/ul>\n<p>un r\u00f4le dans le d\u00e9veloppement de la maladie. La SLA progresse g\u00e9n\u00e9ralement lentement et affecte progressivement d\u2019autres parties du corps. Elle est consid\u00e9r\u00e9e comme incurable. <\/p>\n<\/div>\n<div data-hk=\"00942120a20290\" class=\"Html-Block\" data-qa-article-content-text>\n<p>La maladie d\u00e9bute g\u00e9n\u00e9ralement entre 50 et 70 ans. Les hommes sont plus souvent touch\u00e9s que les femmes. Il y a actuellement environ 8 000 \u00e0 9 000 patients en Allemagne ; Chaque ann\u00e9e, environ 2 500 personnes dans ce pays re\u00e7oivent un nouveau diagnostic de SLA, \u00e9crit le DZNE.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202a1004\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-3\" data-orientation=\"hor\" data-index=\"3\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a202a110\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Les causes des maladies neurod\u00e9g\u00e9n\u00e9ratives restent floues<\/h2>\n<p>L&rsquo;esp\u00e9rance de vie moyenne apr\u00e8s le diagnostic est de trois \u00e0 quatre ans. Cependant, des progressions nettement plus lentes sur dix ans ou plus sont \u00e9galement connues. <\/p>\n<\/div>\n<div data-hk=\"00942120a202a120\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Les raisons de la plupart des cas de SLA restent floues. Chez environ cinq pour cent des personnes touch\u00e9es, la maladie est g\u00e9n\u00e9tique et h\u00e9r\u00e9ditaire.  <\/p>\n<\/div>\n<div data-hk=\"00942120a202a130\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Comment la SLA est diagnostiqu\u00e9e<\/h2>\n<p>La SLA est diagnostiqu\u00e9e lors d&rsquo;un examen clinique par un neurologue. Les muscles sont principalement \u00e9valu\u00e9s en ce qui concerne la perte musculaire et les contractions des faisceaux de fibres musculaires. L&rsquo;\u00e9lectromyographie permet de mesurer l&rsquo;activit\u00e9 \u00e9lectrique du muscle au repos et pendant l&rsquo;activit\u00e9 ainsi que la vitesse de conduction nerveuse. <\/p>\n<\/div>\n<aside data-hk=\"00942120a202a1404\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-4\" data-orientation=\"hor\" data-index=\"4\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<aside data-hk=\"00942120a202a1504\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-desktop Ad-Slot-hor Ad-Slot-FC\">\n<div class=\"Ad-Slot-FC-Container\">\n<div class=\"Ad-Slot-FC-Window\">\n<div id=\"ad-slot-desktop-hor-2\" data-orientation=\"hor\" data-index=\"2\" data-slot=\"ad-slot\" data-device=\"desktop\"><\/div>\n<\/div>\n<\/div>\n<\/aside>\n<div data-hk=\"00942120a202a160\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Les fonctions de parole, de d\u00e9glutition et de respiration sont \u00e9galement v\u00e9rifi\u00e9es. Afin d\u2019exclure des maladies similaires, le neurologue examine \u00e9galement les fonctions du syst\u00e8me nerveux qui ne sont pas affect\u00e9es par la SLA. En outre, les examens d&rsquo;\u00e9chantillons de sang, d&rsquo;urine et d&rsquo;eau nerveuse font partie du diagnostic, tout comme les proc\u00e9dures d&rsquo;imagerie telles que l&rsquo;IRM et la tomodensitom\u00e9trie.<\/p>\n<\/div>\n<div data-hk=\"00942120a202a170\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Traitement de la SLA<\/h2>\n<p>Les causes de la SLA \u00e9tant encore inconnues, il n\u2019existe actuellement aucun traitement permettant de gu\u00e9rir la maladie. <\/p>\n<\/div>\n<div data-hk=\"00942120a202a180\" class=\"Html-Block\" data-qa-article-content-text>\n<p>\u00c0 ce jour, il n\u2019existe qu\u2019un seul m\u00e9dicament approuv\u00e9 pour le traitement de la SLA : le riluzole. Cela peut prolonger quelque peu l\u2019esp\u00e9rance de vie. Les chercheurs sont \u00e9galement constamment \u00e0 la recherche de nouvelles th\u00e9rapies.<\/p>\n<\/div>\n<div data-hk=\"00942120a202a190\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Il existe \u00e9galement des options de traitement visant \u00e0 soulager les sympt\u00f4mes. Cela comprend la physioth\u00e9rapie et l\u2019entra\u00eenement aux fonctions respiratoires, vocales et de d\u00e9glutition.<\/p>\n<\/div>\n<p><!--\/--><br \/>\n<!--$--><br \/>\n<!--\/--><br \/>\n<!--$--><br \/>\n<!--\/--><\/p>\n","protected":false},"excerpt":{"rendered":"<p>dans la vid\u00e9o : La star de \u00ab\u00a0Grey&rsquo;s Anatomy\u00a0\u00bb, Eric Dane, d\u00e9c\u00e8de \u00e0 seulement 53<\/p>\n","protected":false},"author":1,"featured_media":14302,"comment_status":"open","ping_status":"","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[86],"tags":[2454,2023,8979,248,8978,20,193,8980],"class_list":["post-14301","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-les-maladies","tag-cache","tag-derriere","tag-incurable","tag-maladie","tag-nerveuse","tag-questce","tag-qui","tag-sla","generate-columns","tablet-grid-50","mobile-grid-100","grid-parent","grid-50","resize-featured-image"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.4 - 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