{"id":13840,"date":"2026-02-05T12:10:48","date_gmt":"2026-02-05T11:10:48","guid":{"rendered":"https:\/\/rvh-synergie.org\/actualites\/neurolupus-quand-le-systeme-immunitaire-attaque-le-cerveau\/"},"modified":"2026-02-05T12:10:49","modified_gmt":"2026-02-05T11:10:49","slug":"neurolupus-quand-le-systeme-immunitaire-attaque-le-cerveau","status":"publish","type":"post","link":"https:\/\/rvh-synergie.org\/actualites\/neurolupus-quand-le-systeme-immunitaire-attaque-le-cerveau\/","title":{"rendered":"Neurolupus : Quand le syst\u00e8me immunitaire attaque le cerveau"},"content":{"rendered":"<p><!--$--><\/p>\n<div data-hk=\"00942120a20200\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Le lupus \u00e9ryth\u00e9mateux syst\u00e9mique (LED) est consid\u00e9r\u00e9 comme l\u2019une des maladies auto-immunes les plus complexes de la m\u00e9decine moderne. De nombreuses personnes connaissent la maladie, principalement \u00e0 cause de douleurs articulaires, d&rsquo;\u00e9ruptions cutan\u00e9es ou de probl\u00e8mes r\u00e9naux. <\/p>\n<\/div>\n<div data-hk=\"00942120a20210\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Cependant, le public est moins conscient de l\u2019une des complications les plus graves : l\u2019atteinte du syst\u00e8me nerveux central (SNC). Les m\u00e9decins parlent alors de <strong>lupus \u00e9ryth\u00e9mateux syst\u00e9mique neuropsychiatrique (NPSLE)<\/strong> \u2013 une forme qui pose de grands d\u00e9fis aux personnes touch\u00e9es et \u00e0 ceux qui les soignent.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202204\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor Ad-Slot-FC\">\n<div class=\"Ad-Slot-FC-Container\">\n<div class=\"Ad-Slot-FC-Window\">\n<div id=\"ad-slot-mobile-hor-2\" data-orientation=\"hor\" data-index=\"2\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/div>\n<\/div>\n<\/aside>\n<div data-hk=\"00942120a20230\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Un tableau clinique diversifi\u00e9<\/h2>\n<p>Le LED est une maladie auto-immune inflammatoire chronique qui touche principalement les jeunes femmes. La cause est une r\u00e9action immunitaire erron\u00e9e : le corps forme des auto-anticorps qui attaquent ses propres tissus et peuvent d\u00e9clencher une inflammation dans presque tous les organes. Le cerveau et la moelle \u00e9pini\u00e8re ne sont pas non plus \u00e9pargn\u00e9s.<\/p>\n<\/div>\n<div data-hk=\"00942120a20240\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Il est apparu tr\u00e8s t\u00f4t que les sympt\u00f4mes neurologiques et psychiatriques du LED peuvent varier consid\u00e9rablement \u2013 \u200b\u200bdepuis de l\u00e9gers probl\u00e8mes de concentration jusqu&rsquo;\u00e0 de graves accidents vasculaires c\u00e9r\u00e9braux ou une inflammation de la moelle \u00e9pini\u00e8re. Afin de capturer syst\u00e9matiquement cette diversit\u00e9, l\u2019American College of Rheumatology a d\u00e9velopp\u00e9 une classification de 19 syndromes neuropsychiatriques clairement d\u00e9finis pouvant \u00eatre attribu\u00e9s au lupus.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202504\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-out\">\n<div id=\"ad-slot-mobile-out-1\" data-orientation=\"out\" data-index=\"1\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a20260\" class=\"Ad-Row\">\n<div class=\"Ad-Col col-lg-5\">\n<div data-hk=\"00942120a2026104\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-desktop Ad-Slot-ver\" role=\"region\" aria-label=\"Anzeige 1\">\n<div id=\"ad-slot-desktop-ver-1\" data-orientation=\"ver\" data-index=\"1\" data-slot=\"ad-slot\" data-device=\"desktop\"><\/div>\n<\/div>\n<\/div>\n<div class=\"Ad-Col col-lg-5\">\n<aside data-hk=\"00942120a2026204\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-desktop Ad-Slot-ver Ad-Slot-FC\">\n<div class=\"Ad-Slot-FC-Container\">\n<div class=\"Ad-Slot-FC-Window\">\n<div id=\"ad-slot-desktop-ver-2\" data-orientation=\"ver\" data-index=\"2\" data-slot=\"ad-slot\" data-device=\"desktop\"><\/div>\n<\/div>\n<\/div>\n<\/aside>\n<\/div>\n<\/div>\n<div data-hk=\"00942120a20270\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>\u00c0 quelle fr\u00e9quence le syst\u00e8me nerveux central est-il affect\u00e9 ?<\/h2>\n<p>La fr\u00e9quence d\u2019apparition du NPSLE fait encore l\u2019objet de recherches intensives. Les informations varient consid\u00e9rablement : dans les \u00e9tudes, elles vont de moins de cinq \u00e0 plus de 90 pour cent. La raison r\u00e9side principalement dans les diff\u00e9rentes d\u00e9finitions. Certaines \u00e9tudes incluent \u00e9galement des sympt\u00f4mes non sp\u00e9cifiques tels que des maux de t\u00eate ou des sautes d\u2019humeur, tandis que d\u2019autres se limitent \u00e0 des \u00e9v\u00e9nements neurologiques graves et clairement d\u00e9montrables.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202804\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-3\" data-orientation=\"hor\" data-index=\"3\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a20290\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Une vaste \u00e9tude de cohorte prospective est parvenue \u00e0 la conclusion qu&rsquo;environ quatre \u00e0 13\u00a0% des patients d\u00e9veloppent une atteinte s\u00e9v\u00e8re et clairement d\u00e9finie du SNC au cours de la maladie. L&rsquo;incidence annuelle \u00e9tait de 7,8 cas pour 100 ann\u00e9es-personnes. Les crises d\u2019\u00e9pilepsie, les accidents vasculaires c\u00e9r\u00e9braux et l\u2019inflammation de la moelle \u00e9pini\u00e8re \u00e9taient particuli\u00e8rement fr\u00e9quents.<\/p>\n<\/div>\n<div data-hk=\"00942120a202a100\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Sympt\u00f4mes focaux ou diffus \u2013 deux faces du neurolupus<\/h2>\n<p>Les manifestations neurologiques du NPSLE peuvent \u00eatre grossi\u00e8rement divis\u00e9es en deux groupes.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202a1104\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-4\" data-orientation=\"hor\" data-index=\"4\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a202a120\" class=\"Html-Block\" data-qa-article-content-text>\n<p><strong>Manifestations focales et organiques<\/strong><\/p>\n<\/div>\n<div data-hk=\"00942120a202a130\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Ceux-ci incluent, entre autres :<\/p>\n<\/div>\n<div data-hk=\"00942120a202a140\" class=\"Html-Block\" data-qa-article-content-text>\n<ol>\n<li>accidents vasculaires c\u00e9r\u00e9braux isch\u00e9miques ou h\u00e9morragiques<\/li>\n<li>my\u00e9lite transverse et autres my\u00e9lopathies<\/li>\n<li>crises d&rsquo;\u00e9pilepsie<\/li>\n<li>m\u00e9ningite aseptique<\/li>\n<\/ol>\n<p>Ces formes peuvent g\u00e9n\u00e9ralement \u00eatre objectiv\u00e9es par des \u00e9tudes d\u2019imagerie ou \u00e9lectrophysiologiques et s\u2019accompagnent souvent de dommages structurels permanents.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202a1504\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-desktop Ad-Slot-hor Ad-Slot-FC\">\n<div class=\"Ad-Slot-FC-Container\">\n<div class=\"Ad-Slot-FC-Window\">\n<div id=\"ad-slot-desktop-hor-2\" data-orientation=\"hor\" data-index=\"2\" data-slot=\"ad-slot\" data-device=\"desktop\"><\/div>\n<\/div>\n<\/div>\n<\/aside>\n<div data-hk=\"00942120a202a160\" class=\"Html-Block\" data-qa-article-content-text>\n<p><strong>Manifestations neuropsychiatriques diffuses<\/strong><\/p>\n<\/div>\n<div data-hk=\"00942120a202a170\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Ceux-ci incluent\u00a0:<\/p>\n<\/div>\n<aside data-hk=\"00942120a202a1804\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-5\" data-orientation=\"hor\" data-index=\"5\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a202a190\" class=\"Html-Block\" data-qa-article-content-text>\n<ol>\n<li>psychoses aigu\u00ebs<\/li>\n<li>\u00c9tats de confusion<\/li>\n<li>limitations cognitives<\/li>\n<li>Troubles d\u00e9pressifs et anxieux<\/li>\n<\/ol>\n<p>Ces sympt\u00f4mes posent particuli\u00e8rement probl\u00e8me aux m\u00e9decins, car ils peuvent \u00e9galement \u00eatre provoqu\u00e9s par des m\u00e9dicaments, des troubles m\u00e9taboliques ou un stress psychosocial. Une attribution claire au lupus est donc souvent difficile.<\/p>\n<\/div>\n<div data-hk=\"00942120a202a200\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Pourquoi le lupus attaque-t-il le cerveau ?<\/h2>\n<p>Le d\u00e9veloppement du NPSLE est complexe. Contrairement aux maladies inflammatoires c\u00e9r\u00e9brales classiques, il n\u2019y a pas d\u2019inflammation vasculaire prononc\u00e9e au premier plan. Les \u00e9tudes d\u2019autopsie montrent plut\u00f4t des dommages aux petits vaisseaux sanguins, des micro-infarctus et des modifications neuronales diffuses.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202a2104\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-6\" data-orientation=\"hor\" data-index=\"6\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a202a220\" class=\"Html-Block\" data-qa-article-content-text>\n<p>Les m\u00e9canismes pathog\u00e8nes les plus importants comprennent\u00a0:<\/p>\n<\/div>\n<div data-hk=\"00942120a202a230\" class=\"Html-Block\" data-qa-article-content-text>\n<ol>\n<li><strong>Autoanticorps<\/strong>comme les anticorps antiphospholipides, qui augmentent le risque d&rsquo;accident vasculaire c\u00e9r\u00e9bral<\/li>\n<li><strong>Anticorps anti-neuronaux<\/strong>qui peut influencer directement les cellules nerveuses<\/li>\n<li><strong>Complexes immunitaires et activation du compl\u00e9ment<\/strong>qui endommagent la barri\u00e8re h\u00e9mato-enc\u00e9phalique<\/li>\n<li><strong>Cytokines inflammatoires<\/strong>qui ont des effets neurotoxiques<\/li>\n<\/ol>\n<p>Ce m\u00e9lange explique pourquoi les processus thrombotiques et inflammatoires jouent un r\u00f4le dans le neurolupus.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202a2404\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-7\" data-orientation=\"hor\" data-index=\"7\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a202a250\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Difficile \u00e0 reconna\u00eetre : le neurolupus comme diagnostic d&rsquo;exclusion<\/h2>\n<p>Le diagnostic du NPSLE est difficile car il n\u2019existe actuellement aucun biomarqueur unique et fiable. C&rsquo;est pourquoi il s&rsquo;agit d&rsquo;un diagnostic classique d&rsquo;exclusion. La norme de diagnostic comprend\u00a0:<\/p>\n<\/div>\n<aside data-hk=\"00942120a202a2604\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-desktop Ad-Slot-out\">\n<div id=\"ad-slot-desktop-out-1\" data-orientation=\"out\" data-index=\"1\" data-slot=\"ad-slot\" data-device=\"desktop\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a202a270\" class=\"Html-Block\" data-qa-article-content-text>\n<ol>\n<li>un examen neurologique et psychiatrique approfondi<\/li>\n<li>une imagerie par r\u00e9sonance magn\u00e9tique (IRM) du cerveau et de la moelle \u00e9pini\u00e8re<\/li>\n<li>un EEG si une activit\u00e9 \u00e9pileptique est suspect\u00e9e<\/li>\n<li>un examen du liquide c\u00e9phalo-rachidien pour exclure toute infection<\/li>\n<li>profils s\u00e9rologiques d\u2019autoanticorps<\/li>\n<\/ol>\n<p>Il est particuli\u00e8rement important de diff\u00e9rencier les infections, les effets secondaires des m\u00e9dicaments ou les troubles m\u00e9taboliques, qui surviennent souvent chez les patients immunod\u00e9prim\u00e9s lupiques.<\/p>\n<\/div>\n<aside data-hk=\"00942120a202a2804\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-8\" data-orientation=\"hor\" data-index=\"8\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a202a290\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Comment traite-t-on le neurolupus ?<\/h2>\n<p>Le traitement du NPSLE repose principalement sur l\u2019exp\u00e9rience clinique, car les grandes \u00e9tudes randomis\u00e9es sont rares. Les piliers les plus importants comprennent\u00a0:<\/p>\n<\/div>\n<div data-hk=\"00942120a202a300\" class=\"Html-Block\" data-qa-article-content-text>\n<ol>\n<li><strong>glucocortico\u00efdes \u00e0 haute dose<\/strong> dans les manifestations inflammatoires<\/li>\n<li><strong>Immunosuppresseurs<\/strong> comme le cyclophosphamide ou l&rsquo;azathioprine dans les cas graves<\/li>\n<li><strong>Produits biologiques<\/strong>en particulier le rituximab, dans les cas r\u00e9sistants au traitement<\/li>\n<\/ol>\n<p>En cas d&rsquo;\u00e9v\u00e9nements thrombotiques, une m\u00e9dication constante pour inhiber la coagulation sanguine (anticoagulation) est \u00e9galement n\u00e9cessaire. L\u2019objectif est de contr\u00f4ler l\u2019inflammation aigu\u00eb et de pr\u00e9venir les dommages neurologiques \u00e0 long terme <\/p>\n<\/div>\n<aside data-hk=\"00942120a202a3104\" data-qa-ad-slot class=\"Ad-Slot Ad-Slot-mobile Ad-Slot-hor\">\n<div id=\"ad-slot-mobile-hor-9\" data-orientation=\"hor\" data-index=\"9\" data-slot=\"ad-slot\" data-device=\"mobile\"><\/div>\n<\/aside>\n<div data-hk=\"00942120a202a320\" class=\"Html-Block\" data-qa-article-content-text>\n<h2>Pr\u00e9visions et perspectives<\/h2>\n<p>Le pronostic du neurolupus varie consid\u00e9rablement. M\u00eame si les sympt\u00f4mes disparaissent compl\u00e8tement chez certaines personnes touch\u00e9es, il n&rsquo;est pas rare que des d\u00e9ficits neurologiques permanents persistent apr\u00e8s des cas graves. Dans l&rsquo;ensemble, l&rsquo;implication du SNC contribue de mani\u00e8re significative au fardeau de la maladie et \u00e0 la mortalit\u00e9 li\u00e9e au LED.<\/p>\n<\/div>\n<div data-hk=\"00942120a202a330\" class=\"Html-Block\" data-qa-article-content-text>\n<p>La recherche se concentre de plus en plus sur des biomarqueurs sp\u00e9cifiques et des th\u00e9rapies immunomodulatrices cibl\u00e9es qui pourraient permettre un diagnostic plus pr\u00e9coce et un traitement plus individualis\u00e9 \u00e0 l&rsquo;avenir. Jusque-l\u00e0, le neurolupus reste l\u2019un des plus grands d\u00e9fis de la rhumatologie et de la neurologie modernes.<\/p>\n<\/div>\n<div data-hk=\"00942120a202a340\" class=\"Article-ReusableText Html-Block\" data-qa-article-reusable-content-text>\n<p>Dr m\u00e9d. Mimoun Azizi est m\u00e9decin-chef du Centre de g\u00e9riatrie et de neurog\u00e9riatrie du KVSW et sp\u00e9cialiste en neurologie. Il fait partie de notre Cercle EXPERTS. Le contenu repr\u00e9sente son opinion personnelle bas\u00e9e sur son expertise individuelle.<\/p>\n<\/div>\n<p><!--\/--><br \/>\n<!--$--><br \/>\n<!--\/--><br \/>\n<!--$--><br \/>\n<!--\/--><script async src=\"\/\/www.instagram.com\/embed.js\"><\/script><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Le lupus \u00e9ryth\u00e9mateux syst\u00e9mique (LED) est consid\u00e9r\u00e9 comme l\u2019une des maladies auto-immunes les plus complexes<\/p>\n","protected":false},"author":1,"featured_media":13841,"comment_status":"open","ping_status":"","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[86],"tags":[5627,585,834,8783,6903,843],"class_list":["post-13840","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-les-maladies","tag-attaque","tag-cerveau","tag-immunitaire","tag-neurolupus","tag-quand","tag-systeme","generate-columns","tablet-grid-50","mobile-grid-100","grid-parent","grid-50","resize-featured-image"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.4 - 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