{"id":1076,"date":"2024-10-05T15:05:45","date_gmt":"2024-10-05T13:05:45","guid":{"rendered":"https:\/\/rvh-synergie.org\/actualites\/comprendre-la-fibrose-hepatique-apercus-du-syndrome-dalagille\/"},"modified":"2024-10-05T15:05:51","modified_gmt":"2024-10-05T13:05:51","slug":"comprendre-la-fibrose-hepatique-apercus-du-syndrome-dalagille","status":"publish","type":"post","link":"https:\/\/rvh-synergie.org\/actualites\/comprendre-la-fibrose-hepatique-apercus-du-syndrome-dalagille\/","title":{"rendered":"Comprendre la fibrose h\u00e9patique\u00a0: aper\u00e7us du syndrome d&rsquo;Alagille"},"content":{"rendered":"<div>\n<div class=\"article-gallery lightGallery\">\n<div data-thumb=\"https:\/\/scx1.b-cdn.net\/csz\/news\/tmb\/2024\/understanding-liver-fi.jpg\" data-src=\"https:\/\/scx2.b-cdn.net\/gfx\/news\/hires\/2024\/understanding-liver-fi.jpg\" data-sub-html=\"Jag1&lt;sup&gt;Ndr\/Ndr&lt;\/sup&gt; mice display pericellular fibrosis and signs of portal hypertension. Credit: &lt;i&gt;EMBO Molecular Medicine&lt;\/i&gt; (2024). DOI: 10.1038\/s44321-024-00145-8\">\n<figure class=\"article-img\">\n<\/figure><\/div>\n<\/div>\n<p>Qu\u2019est-ce qui influence l\u2019\u00e9tendue du tissu cicatriciel, ou fibrose, qui se d\u00e9veloppe dans le foie lorsque les personnes souffrent d\u2019une maladie du foie ? M\u00eame si une petite quantit\u00e9 de fibrose fait normalement partie du processus de gu\u00e9rison, une fibrose excessive peut survenir, entra\u00eenant des complications et, finalement, une insuffisance h\u00e9patique. Comprendre les m\u00e9canismes \u00e0 l\u2019origine de cette escalade est essentiel dans la lutte contre les maladies du foie.<\/p>\n<p>Pour r\u00e9pondre \u00e0 cette question, des chercheurs du Karolinska Institutet et de l&rsquo;Universit\u00e9 Charles ont \u00e9tudi\u00e9 une maladie g\u00e9n\u00e9tique appel\u00e9e syndrome d&rsquo;Alagille, caract\u00e9ris\u00e9e par une fibrose h\u00e9patique \u00e9tonnamment l\u00e9g\u00e8re malgr\u00e9 une maladie h\u00e9patique grave (fibrose p\u00e9ricellulaire au lieu de pontage).<\/p>\n<p>En employant le s\u00e9quen\u00e7age d\u2019ARN unicellulaire et en transplantant des cellules immunitaires du mod\u00e8le murin dans un mod\u00e8le diff\u00e9rent de maladie du foie, l\u2019\u00e9quipe a d\u00e9couvert que le syst\u00e8me immunitaire des patients atteints du syndrome d\u2019Alagille joue un r\u00f4le dans la suppression de la formation de tissu cicatriciel dans le foie.<\/p>\n<p>\u00ab\u00a0Nous pensons que ces r\u00e9sultats pourraient avoir des implications plus larges pour le traitement de la fibrose h\u00e9patique, potentiellement gr\u00e2ce \u00e0 une manipulation cibl\u00e9e du syst\u00e8me immunitaire\u00a0\u00bb, d\u00e9clarent Emma Andersson et Jan Ma\u0161ek, qui ont dirig\u00e9 l&rsquo;\u00e9quipe de chercheurs internationaux.<\/p>\n<p>L&rsquo;article est publi\u00e9 dans la revue <i>EMBO M\u00e9decine Mol\u00e9culaire<\/i>.<\/p>\n<p>Le Dr Jan Ma\u0161ek a commenc\u00e9 ce projet alors qu&rsquo;il effectuait un post-doctorat dans le laboratoire du Dr Emma Andersson au D\u00e9partement de biologie cellulaire et mol\u00e9culaire du Karolinska Institutet. Le projet s&rsquo;est poursuivi sous forme de collaboration, une fois que le Dr Ma\u0161ek a cr\u00e9\u00e9 son propre laboratoire \u00e0 l&rsquo;Universit\u00e9 Charles en R\u00e9publique tch\u00e8que.<\/p>\n<p>Des collaborations cruciales avec des immunologistes de l&rsquo;\u00e9quipe du professeur Niklas Bj\u00f6rkstr\u00f6m du d\u00e9partement de m\u00e9decine de Huddinge, du Karolinska Institutet, du laboratoire du Dr Jan Dobes \u00e0 l&rsquo;Universit\u00e9 Charles et des h\u00e9patologues du laboratoire du Dr Martin Gregor \u00e0 l&rsquo;Institut de g\u00e9n\u00e9tique mol\u00e9culaire de Prague ont \u00e9t\u00e9 inestimables. concr\u00e9tiser cette recherche interdisciplinaire.<\/p>\n<p>                                        <!-- print only --><\/p><\/div>\n","protected":false},"excerpt":{"rendered":"<p>Qu\u2019est-ce qui influence l\u2019\u00e9tendue du tissu cicatriciel, ou fibrose, qui se d\u00e9veloppe dans le foie<\/p>\n","protected":false},"author":1,"featured_media":1077,"comment_status":"closed","ping_status":"","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[86],"tags":[1392,310,1393,654,655,283],"class_list":["post-1076","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-les-maladies","tag-apercus","tag-comprendre","tag-dalagille","tag-fibrose","tag-hepatique","tag-syndrome","generate-columns","tablet-grid-50","mobile-grid-100","grid-parent","grid-50","resize-featured-image"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.4 - 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